A Case of Congenital Reddish Neurofibromatous Dermal Hypoplasia

A 17-year-old Korean boy with neurofibromatosis (NF) type 1 showed well-demarcated congenital reddish atrophic patches with follicular papules on the abdomen and left thigh. Results of a histologic examination of an atrophic patch showed collagen reduction in the reticular dermis with neuroid cuffs around thick-walled blood vessels. Dermatologists should be aware of this uncommon clinical finding of NF because it may be useful for early diagnosis.